Giant fibrosarcoma arising in dermatofibrosarcoma protuberans on the scalp during pregnancy

Dermatofibrosarcoma protuberans (DFSP) is a low-grade malignant soft tissue tumor of subcutaneous tissues that has a propensity for local recurrence; however, it seldom metastasizes. Most lesions occur over the trunk or proximal extremities, and there is slight male preponderance. DFSP is rare on the head and neck. Less than 5% tumors are located on the scalp. OBJECTIVE. To describe a case of giant fibrosarcoma arising in DFSP on the scalp during pregnancy. METHOD. In our patient, the tumor was on scalp and measured 15 11 7 cm. The recurrent tumor that developed in the same region was measured 33 30 15 cm. Histopathologic examination of this mass revealed fibrosarcoma. The mass was excised from the subperiosteal plane with a 3-cm free margin. Because of the high possibility of recurrence, the defect site was reconstructed with a split-thickness skin graft. RESULTS. After 1 year of follow-up, no recurrence or metastasis was detected.